One of the treatments for hemophilia is more of a therapeutic and that is when we administer replacement clotting factors. So, that’s the next goal of ours; we want to replace clotting factors and that’s just an infusion that we can give IV. Replacing clotting factors is the primary treatment for hemophilia.
Full Answer
What does the nurse notice while caring for a patient with hemophilia?
What treatment does the nurse expect a patient diagnosed with hemophilia to receive? Synthetic factor VIII A 56-year-old patient admitted with a diagnosis of acute myelogenous leukemia (AML) is prescribed intravenous cytosine arabinoside for 7 …
What is the treatment for hemophilia A?
A patient with multiple myeloma is being cared for at home. Which nursing diagnosis should guide the nurse when teaching the family how to provide care for the patient? a. Risk for Injury related to compromised bone integrity b. Ineffective Tissue Perfusion related to vascular occlusion c. Risk for Deficient Fluid Volume related to bleeding ...
How is hemophilia diagnosed?
Oct 07, 2021 · Treatment. The main treatment for severe hemophilia involves replacing the clotting factor you need through a tube in a vein. This replacement therapy can be given to treat a bleeding episode in progress. It can also be given on a regular schedule at home to help prevent bleeding episodes. Some people receive continuous replacement therapy.
Which is an appropriate measure to control bleeding in hemophilia?
Apply pressure to site for several minutes to allow time to clot. Administer medications orally as available; administer replacement clotting factors as necessary. Replacement of clotting factors is the primary treatment for hemophilia; other supplements, antibodies and …
Which nursing intervention would be appropriate in the care of a patient diagnosed with immune thrombocytopenic purpura?
Which type of therapy will the nurse anticipate administering to a patient who has newly diagnosed Helicobacter pylori?
Triple H. pylori therapy comprising a PPI, amoxicillin and clarithromycin is used as the firstline therapy.Jan 16, 2016
Which therapy would be beneficial for a patient who experiences a minor bleeding episode during a dental procedure?
Which blood product may be administered to a patient diagnosed with thrombotic thrombocytopenic purpura?
Which medication is used to treat Helicobacter pylori infection?
Which medication is used to treat Helicobacter pylori infection select all that apply?
| Type | Regimen | Eradication rate |
|---|---|---|
| First line | ||
| Standard triple therapy | PPI, amoxicillin 1 g, and clarithromycin 500 mg (Biaxin) twice daily | 70% to 85% |
| PPI, clarithromycin 500 mg, and metronidazole 500 mg (Flagyl) twice daily | 70% to 85% | |
What is the specific intranasal treatment therapy used prior to a dental or minor surgical procedure for a mild hemophiliac patient?
When preparing to administer a prescribed blood transfusion the nurse should select which intravenous IV solution to prime the blood tubing?
Which effect does desmopressin acetate have on clotting factors?
Which is the treatment of choice for thrombotic thrombocytopenic purpura TTP?
Which medication may be given for treatment of heparin induced thrombocytopenia select all that apply?
How do you treat TMA?
How to treat hemophilia?
Treatment of Hemophilia. The best way to treat hemophilia is to replace the missing blood clotting factor so that the blood can clot properly. This is typically done by injecting treatment products, called clotting factor concentrates, into a person’s vein. Clinicians typically prescribe treatment products for episodic care or prophylactic care.
Is hemophilia a complex disorder?
Hemophilia is a complex disorder. Good quality medical care from doctors and nurses who know a lot about the disorder can help people with hemophilia prevent some serious problems. Often the best choice for care is at a comprehensive hemophilia treatment center (HTC).
Can you give clotting factor at home?
Today, it’s possible for people with hemophilia, and their families, to learn how to give their own clotting factor treatment products at home. Giving factor treatment products at home means that bleeds can be treated quicker, resulting in less serious bleeding and fewer side effects.
What is HTC care?
An HTC provides patients with the care and education to address all issues related to the disorder. The team consists of physicians (hematologists or blood specialists), nurses, social workers, physical therapists, and other healthcare providers who are specialized in the care of people with bleeding disorders.
Is factor VIII made from human plasma?
Until 1992, all factor replacement products were made from human plasma. In 1992, the U.S. Food and Drug Administration (FDA) approved recombinant factor VIII (8) concentrate, which does not come from human plasma. This concentrate is genetically engineered using DNA technology. Commercially prepared factor concentrates are treated to remove or inactivate bloodborne viruses. Additionally, recombinant factors VIII (8) and IX (9) do not contain any plasma or albumin, and therefore, cannot spread any bloodborne viruses.
How does hemlibra work?
Hemlibra ® works by replacing the function of factor VIII (8) , rather than replacing the missing clotting factor VIII directly. It can be used to either prevent or reduce the frequency of bleeding episodes in people with hemophilia A. This treatment product can be given by injection under the skin. Patients who use Hemlibra ® for prophylaxis and use clotting factor concentrates to treat breakthrough bleeds, can still develop an inhibitor. Traditional laboratory inhibitor testing methods do not work when testing for inhibitors in patients on Hemlibra ®; as such, a specialized testing method called the chromogenic Bethesda assay is needed.
How does DDAVP work?
For people with mild, as well as some cases of moderate, hemophilia, this can work to increase the persons own factor VIII (8) levels so that they do not have to use clotting factors to stop bleeding episodes. DDAVP ® can be given through a vein and Stimate ® .via a nasal spray.
What is the treatment for hemophilia?
The treatment of hemophilia may involve prophylaxis, management of bleeding episodes, treatment of factor VIII (FVIII) inhibitors, and treatment and rehabilitation of hemophilia synovitis. Ryan White was an American hemophiliac who was infected with HIV from a contaminated blood treatment (factor VIII).
Can hemophilia be avoided?
Generally, individuals with severe hemophilia should avoid high-impact contact sports and other activities with a significant risk of trauma; however, mounting evidence suggests that appropriate physical activity improves overall conditioning, reduces injury rate and severity, and improves psychosocial functioning.
What is the genetic disorder that causes blood clots?
Hemophilia is an inherited, genetic disorder that hinders the body’s ability to form blood clots, a process necessary to halt bleeding. Hemophilia results from mutations at the factor VIII or IX loci on the X chromosome and each occurs in mild, moderate, and severe forms. A similar level of deficiency of factor VIII or IX results in clinically ...
Where does hemophilia occur?
Hemophilia results from mutations at the factor VIII or IX loci on the X chromosome and each occurs in mild, moderate, and severe forms.
Is hemophilia a recessive disorder?
Hemophilia A is an X-linked, recessive disorder caused by the deficiency of functional plasma clotting factor VIII (FVIII), which may be inherited or arise from spontaneous mutation. Hemophilia B, or Christmas disease, is an inherited, X-linked, recessive disorder that results in the deficiency of functional plasma coagulation factor IX.
What is factor IX deficiency?
Factor IX deficiency, dysfunctional factor IX, or factor IX inhibitors lead to disruption of the normal intrinsic coagulation cascade, resulting in spontaneous hemorrhage and/or excessive hemorrhage in response to trauma.
How common is hemophilia A?
Hemophilia A is the most common X-linked genetic disease and the second most common factor deficiency after von Willebrand disease (vWD). The worldwide incidence of hemophilia A is approximately 1 case per 5000 males, with approximately one-third of affected individuals not having a family history of the disorder.
How long does a platelet last?
Each platelet has a life span of 1 to 2 weeks. Chronologically arrange the events involved in bone marrow aspiration chronologically. Bone marrow aspiration is performed if the hematological assessment is inappropriate in general blood tests. In this procedure, the test site is first cleaned by disinfectant.
Where are platelets produced?
Platelets are produced in the bone marrow. Each platelet has a life span of 1 to 2 weeks. Chronologically arrange the events involved in bone marrow aspiration chronologically. Bone marrow aspiration is performed if the hematological assessment is inappropriate in general blood tests.
What is sickle cell anemia?
Sickle cell anemia is characterized by sickle-shaped RBCs. A patient with anemia and a nursing diagnosis of activity intolerance due to tissue hypoxia and dyspnea is attempting to increase activity tolerance.
What vitamins are needed for anemia?
ANS: A. Iron, folic acid, and vitamin B12 are all essential to production of healthy RBCs. A deficiency of any of these nutrients can cause anemia. B, C, and D are not associated with anemia. A patient with iron-deficiency anemia has been taking oral iron supplements.
Does iron cause anemia?
Iron, folic acid, and vitamin B12 are all essential to production of healthy RBCs. A deficiency of any of these nutrients can cause anemia. B, C, and D are not associated with anemia. A patient with iron-deficiency anemia has been taking oral iron supplements.
What is WBC count?
WBC counts are used to monitor the effectiveness of antibiotic therapy for infections. Platelets are monitored to determine clotting ability. The nurse is assisting in the development of a care plan for a patient with anemia.
When is hemophilia diagnosed?
Depending on the severity of the deficiency, hemophilia symptoms can first arise at various ages. Severe cases of hemophilia usually are diagnosed within the first year of life.
How to help a child with hemophilia?
To help you and your child cope with hemophilia: Get a medical alert bracelet. This bracelet lets medical personnel know that you or your child has hemophilia, and the type of clotting factor that's best in case of an emergency. Talk with a counselor.
Can you test for hemophilia during pregnancy?
For people with a family history of hemophilia, it's possible to determine during pregnancy if the fetus is affected by hemophilia. However, the testing poses some risks to the fetus. Discuss the benefits and risks of testing with your doctor. In children and adults, a blood test can reveal a clotting-factor deficiency.
What is the best treatment for internal bleeding?
Fibrin sealants. These medications can be applied directly to wound sites to promote clotting and healing. Fibrin sealants are especially useful in dental therapy. Physical therapy. It can ease signs and symptoms if internal bleeding has damaged your joints.
How to treat internal bleeding?
If internal bleeding has caused severe damage, you may need surgery. First aid for minor cuts. Using pressure and a bandage will generally take care of the bleeding. For small areas of bleeding beneath the skin, use an ice pack.
How to stop bleeding in mouth?
Using pressure and a bandage will generally take care of the bleeding. For small areas of bleeding beneath the skin, use an ice pack. Ice pops can be used to slow down minor bleeding in the mouth. Vaccinations. Although blood products are screened, it's still possible for people who rely on them to contract diseases.
How to prevent hemophilia?
Lifestyle and home remedies. To avoid excessive bleeding and protect your joints: Exercise regularly. Activities such as swimming, bicycle riding and walking can build up muscles while protecting joints. Contact sports — such as football, hockey or wrestling — are not safe for people with hemophilia.
What is the primary treatment for hemophilia?
Replacement of clotting factors is the primary treatment for hemophilia; other supplements, antibodies and antifibrinolytics may be required. Educate patient and caregivers on safety and prevention of injury.
What are the three levels of hemophilia?
The amount of clotting protein available in the blood determines the severity of hemophilia and categorizes it into three levels: mild, moderate and severe . Complications of the disease include bleeding into the joints, hemorrhage into the central nervous system or vital organs, and aspiration from bleeding into the airways.
What is the genetic disorder of hemophilia?
Hemophilia is a genetic bleeding disorder that is characterized by a deficiency of clotting protein. Patients with hemophilia experience longer bleeding time than others because their blood clots much slower. The amount of clotting protein available in the blood determines the severity of hemophilia and categorizes it into three levels: mild, ...
What is the most common type of hemophilia?
There are two types of hemophilia. Type A (classic) is caused by a deficiency of Factor VIII (8) clotting protein and is the most common, affecting 1 in every 10,000 males. Type B (Christmas disease) is caused by a deficiency of Factor IX (9) and affects 1 in every 30,000 males.
Can bruising cause bleeding?
The deep bruising may lead to bleeding into joint spaces and vital organs. Assess patient for evidence of pain (non-verbal cues) Patients may report painful joints or aching muscles; younger children may not know how to express pain and exhibit symptoms through guarding or irritability and fussiness.
Is hemophilia a recessive disorder?
So let’s recap really quickly. Hemophilia is an x-linked recessive disorder where the patient is missing a clotting factor and therefore bleeds for longer when injured.
What are the symptoms of GI bleeding?
These can be life threatening so make sure not to miss symptoms like 1) Visual Changes 2) Headaches 3) Changes in their level of consciousness 4) Slurred speech. For GI Bleeds be on the lookout for 1) Hematemesis (vomiting blood) and 2) Melena (blood in stools- dark red or black).
What is a pediatrics course?
The Pediatrics Course offers a glimpse into diseases that commonly affect children. Caring for a child requires a different approach to care and prioritization . We help walk you through how to assess a child and how to educate parents on prevention of major illnesses. We break down the diseases into different body systems to help provide clarity and make them easier to understand. This course will help you to confidently care for children of all ages, regardless of what they’re going through.
What Is Hemophilia?
Pathophysiology
Statistics and Incidences
Causes
Clinical Manifestations
Assessment and Diagnostic Findings
Medical Management
- The treatment of hemophilia may involve prophylaxis, management of bleeding episodes, treatment of factor VIII (FVIII) inhibitors, and treatment and rehabilitation of hemophilia synovitis. 1. Prehospital care.Rapid transport to definitive care is the mainstay of prehospital care; prehospital care providers should apply aggressive hemostatic techniq...
Practice Quiz: Hemophilia